Differential diagnoses for IgG₄-related disease

Immunoglobulin G4 (IgG₄)–related disease is an important differential diagnosis for many diseases, includingKhosroshahi, 2015:

• inflammatory connective tissue disease (eg Sjögren syndrome)
• inflammatory bowel disease
• systemic vasculitides
• infectious disease (eg abscess)
• malignant disease (eg pancreatic cancer, cholangiocarcinoma, lymphoma)
• sarcoidosis
• primary sclerosing cholangitis
• type 2 (primary) autoimmune pancreatitis.