Idiopathic nonspecific interstitial pneumonia in adults

Radiologically, idiopathic nonspecific interstitial pneumonia is indistinguishable from nonspecific interstitial pneumonia due to other causes (eg connective tissue disease or drug exposure).

Treatment is generally reserved for patients with severe or progressive disease. First-line therapy includes corticosteroids, with or without steroid-sparing drugs. Smoking cessation is recommended; see Smoking cessation.